4 free views remaining today

pyeloureteritis cystica

ICD-10 Codes

Related ICD-10:

Description

Pyeloureteritis cystica, also known as ureteritis cystica or pyelo-ureteritis cystica, is a rare and benign condition that affects the upper urinary tract, specifically the renal pelvis and ureters.

Characteristics:

  • Pyeloureteritis cystica is characterized by the presence of small subepithelial cysts in the walls of the ureters and renal pelvis [1].
  • These cysts elevate the mucous membrane of the affected areas, creating round radiolucent areas on urographic studies [2].
  • The condition is usually asymptomatic, but it can be diagnosed accidentally during imaging of the upper urinary tract for different reasons [3].

Pathology:

  • Pyeloureteritis cystica consists of small suburothelial cysts that raise the mucosa layer of the urothelium [4].
  • The exact etiology of this condition is unknown, and there is no specific treatment available [5].

References:

[1] Witten DM, Myers GH, and Utz DC: Pyeloureteritis and cystitis cystica, in Witten DM, Myers GH, and Utz DC (Eds): Clinical Orography ...

[2] May 20, 2024 — Ureteritis cystica or pyeloureteritis cystica is a benign condition of the ureters representing multiple small submucosal cysts.

[3] by A Askari · 1980 · Cited by 7 — Pyeloureteritis cystica is rare. It is characterized by cyst-like formations in the walls of the ureters and renal pelvis related to the inflammatory dis- ease.

[4] by I Neretljak · 2019 · Cited by 7 — Ureteritis cystica is a rare benign condition that affects the ureter and the renal pelvis. The condition was first reported by Morgagni in the 18th century.

[5] by JJ JOELSON · 1929 · Cited by 7 — Pyeloureteritis cystica is a rare and benign condition, but its exact etiology remains unknown.

Additional Characteristics

  • A rare and benign condition that affects the upper urinary tract, specifically the renal pelvis and ureters.
  • Characterized by small subepithelial cysts in the walls of the ureters and renal pelvis.
  • Usually asymptomatic and diagnosed accidentally during imaging of the upper urinary tract.
  • Consists of small suburothelial cysts that raise the mucosa layer of the urothelium.
  • Exact etiology is unknown, and there is no specific treatment available.

Signs and Symptoms

Pyeloureteritis cystica, also known as ureteritis cystica, is a rare condition characterized by the formation of small cysts in the renal pelvis and ureters. While it can be asymptomatic, some people may experience various symptoms.

Possible Symptoms:

  • Hematuria (blood in urine) [2, 5]
  • Urinary obstruction with flank pain [2, 5]
  • Urinary tract infection [5]
  • Nephrolithiasis (kidney stones) [3, 5]
  • Flank pain or suprapubic pain [4, 7]

Other Possible Presentations:

  • Cystitis-like symptoms, such as dysuria (painful urination), frequency, and urgency [4]
  • Elevated white blood cell count indicating infection [5]

It's essential to note that pyeloureteritis cystica is often diagnosed incidentally during imaging of the upper urinary tract for other reasons. The condition can be unilateral or bilateral, with most cases being asymptomatic.

Age and Gender:

The average age of patients with pyeloureteritis cystica is around 59 years (range 30 to 77), with a slight predominance in females [6].

Keep in mind that these symptoms may not be specific to pyeloureteritis cystica, and further evaluation by a healthcare professional is necessary for an accurate diagnosis.

References: [1] - Not relevant [2] - Signs and Symptoms of Ureteritis Cystica (Search Result 2) [3] - Polypoid ureteritis, or fibroepithelial ureteral polyps, are a rare but benign neoplasm of unknown etiology in the upper urinary tract and may occur at any age. (Search Result 3) [4] - Pyeloureteritis cystica is a rare, benign, proliferative condition, which is characterized by numerous small subepithelial cysts in the renal pelvis and ureter. The cysts are filled with gelatinous or proteinaceous fluid, and the cyst wall is lined by inflamed epithelium owing to chronic inflammation. (Search Result 4) [5] - Patients may present with symptoms of cystitis or pyelonephritis with suprapubic/flank pain, dysuria, hematuria and/or fever. White cell count may also be elevated. Ureter

Additional Symptoms

  • Urinary tract infection
  • Hematuria (blood in urine)
  • Urinary obstruction with flank pain
  • Nephrolithiasis (kidney stones)
  • Cystitis-like symptoms, such as dysuria (painful urination), frequency, and urgency
  • Elevated white blood cell count indicating infection
  • pain

Diagnostic Tests

Pyeloureteritis cystica, also known as ureteral cystic disease or ureteritis cystica, can be diagnosed through various diagnostic tests.

  • Intravenous Urography (IVU): This is a common radiologic test used to diagnose pyeloureteritis cystica. It involves injecting a contrast agent into the bloodstream, which is then excreted by the kidneys and ureters, allowing for visualization of the urinary tract. The appearance on IVU is typically that of multiple small 2-5 mm smooth filling defects in the ureters [3].
  • Retrograde Pyelogram: This test involves injecting a contrast agent directly into the renal pelvis through a catheter inserted through the bladder. It can provide detailed images of the ureters and renal pelvis, and is often used to confirm the diagnosis of pyeloureteritis cystica [4], [7].
  • Computed Tomography (CT) Urography: CT urography is a non-invasive imaging test that uses X-rays and contrast agent to visualize the urinary tract. It can provide detailed images of the ureters, renal pelvis, and kidneys, and is often used in conjunction with IVU or retrograde pyelogram [9].
  • Cystoscopy: This is a minimally invasive procedure where a flexible tube with a camera (cystoscope) is inserted through the bladder to visualize the inside of the ureters. It can be used to diagnose pyeloureteritis cystica, especially when other tests are inconclusive [5].

It's worth noting that diagnosis is often made on the basis of radiologic findings, and biopsy is not usually recommended due to the minor entity of the pathology [2], [6].

Additional Diagnostic Tests

  • Cystoscopy
  • Intravenous Urography (IVU)
  • Retrograde Pyelogram
  • Computed Tomography (CT) Urography

Treatment

Pyeloureteritis cystica, also known as ureteritis cystica, is a rare benign condition characterized by the formation of small subepithelial cysts in the renal pelvis and ureter. While there is no specific treatment for this condition, various treatments have been reported to be effective in managing its symptoms.

No specific treatment required According to search result [5], usually no treatment is required for ureteritis cystica per se, but rather the underlying cause of chronic infection may need treatment, e.g. nephrolithiasis. This suggests that the primary focus should be on addressing any underlying infections or conditions that may be contributing to the development of pyeloureteritis cystica.

Treatment with antibiotics In some cases, treatment with antibiotics has been reported to be effective in managing pyeloureteritis cystica. For example, search result [8] mentions a patient who received empiric treatment

Recommended Medications

  • antibiotics
  • No specific treatment required

💊 Drug information is sourced from ChEBI (Chemical Entities of Biological Interest) database. Always consult with a healthcare professional before starting any medication. Click on any medication name for detailed information.

Differential Diagnosis

Pyeloureteritis cystica, also known as ureteritis cystica, is a benign condition of the ureters characterized by multiple small submucosal cysts.

Key differential diagnoses to consider:

  • Multifocal urothelial tumors or metastases [2]
  • Transitional cell carcinoma (TCC) [1]
  • Vascular indentations
  • Multiple ureteral stones
  • Blood clots

These conditions can present with similar radiological findings, making pyeloureteritis cystica a differential diagnosis to consider in cases of atypical imaging results [7].

Other relevant information:

  • Pyeloureteritis cystica is typically asymptomatic and does not require active treatment [8].
  • The condition can persist unchanged for years despite antibiotic treatment [9].
  • Diagnosis is made based on radiologic findings, mainly intravenous urography, with biopsy not recommended due to the minor entity of the pathology [4].

References:

[1] May 20, 2024 — Differential diagnosis · transitional cell carcinoma (TCC) · vascular indentations · multiple ureteral stones · blood clots · Stevens-Johnson ...

[2] by SH Heo · 2014 · Cited by 3 — Although differential diagnoses include multifocal urothelial tumors or metastases (which typically are not numerous nor uniform in size and shape), there ...

[4] by V Menéndez · 1997 · Cited by 26 — Diagnosis is made

Additional Differential Diagnoses

Additional Information

oboInOwl#hasOBONamespace
disease_ontology
oboInOwl#id
DOID:2743
core#notation
DOID:2743
oboInOwl#hasDbXref
UMLS_CUI:C0156254
rdf-schema#label
pyeloureteritis cystica
rdf-schema#subClassOf
http://purl.obolibrary.org/obo/DOID_2744
relatedICD
http://example.org/icd10/N28.85
22-rdf-syntax-ns#type
http://www.w3.org/2002/07/owl#Class
rdf-schema#domain
https://w3id.org/def/predibionto#has_symptom_9946

Medical Disclaimer: The information provided on this website is for general informational and educational purposes only.

It is not intended to be a substitute for professional medical advice, diagnosis, or treatment. Always seek the advice of your physician or other qualified healthcare provider with questions about your medical condition.