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pelvic lipomatosis

Description

Pelvic Lipomatosis: A Rare Condition Characterized by Excessive Fat Deposition

Pelvic lipomatosis, also known as pelvic fibrolipomatosis, is a rare and benign condition characterized by an excessive deposition of fat in the pelvis. This leads to compression of surrounding structures such as the bladder, ureter, rectum, and blood vessels.

Key Features:

  • Excessive growth of fat in the pelvic cavity [11]
  • Compression of the bladder, ureter, rectum, and blood vessels [11]
  • Association with proliferative cystitis, such as cystitis cystica [10]
  • Rare condition, with only a few reported cases [8]

Symptoms:

  • Urinary frequency and dysuria (painful urination) [9]
  • Hydronephrosis of the upper urinary tract and renal failure [11]
  • Constipation [11]

Diagnosis:

  • Suggested by radiographic changes on barium enema and intravenous pyelogram [13]
  • Confirmed by surgical biopsy, which reveals fat necrosis [15]

Treatment:

  • Robotic techniques can be used to treat pelvic lipomatosis, with potential difficulties overcoming [8]
  • Surgery may not always be necessary, as the condition is relatively self-limiting [13]

Additional Characteristics

  • Constipation
  • Excessive deposition of fat in the pelvis
  • Compression of surrounding structures such as bladder, ureter, rectum, and blood vessels
  • Association with proliferative cystitis
  • Urinary frequency and dysuria (painful urination)
  • Hydronephrosis of the upper urinary tract and renal failure
  • Fat necrosis on surgical biopsy
  • Potential difficulties in treating pelvic lipomatosis using robotic techniques

Signs and Symptoms

Pelvic lipomatosis is a rare disease characterized by an overgrowth of mature, non-cancerous fat cells in the pelvic region. The symptoms of Pelvic lipomatosis are related to the compression of the urinary system, lower intestinal tract, and vascular system.

Common Symptoms:

  • Obstructive signs and symptoms affecting the genitourinary, digestive, and vascular system [1]
  • Urinary frequency, dysuria, nocturia, and hematuria due to compression of the urinary system [2]
  • Constipation, tenesmus, rectal bleeding, and ribbon-like stools with mucus due to compression of the lower intestinal tract [2]
  • Lumbago, discomfort of the lower abdomen, low-grade fever, recurrent urinary infections, and bladder storage dysfunction symptoms [3][4]
  • Narrowing of the bladder and in some cases also of the rectum as well as distal obstruction of the ureter [5]

Other Possible Symptoms:

  • Pelvic pain
  • Bladder storage dysfunction symptoms
  • Vascular compression leading to symptoms such as lumbago, discomfort of the lower abdomen, low-grade fever, recurrent urinary infections

It's essential to note that these symptoms can vary in severity and may not be present in all cases. If you are experiencing any of these symptoms, it is crucial to consult a healthcare professional for proper diagnosis and treatment.

References: [1] - The clinical features of Pelvic Lipomatosis include obstructive signs and symptoms affecting the genitourinary, digestive, and vascular system... [2] - Pelvic lipomatosis is a rare disease of unknown cause, characterized by overgrowth of mature, non-cancerous fat cells in the pelvic region. [3] - Pelvic lipomatosis is an uncommon benign disease that causes different symptoms due to the compression of pelvic organs by an intrapelvic overgrowth of mature fatty tissue. [4] - Spring 1973 Pelvic lipomatosis 39 fibrosis, (2) metastatic tumor, (3) pelvic retroperitoneal hemorrhage. [5] - Unlike a single lipoma, which is a benign tumor, pelvic lipomatosis can cause compression of the urinary system and lower intestinal tract.

Additional Symptoms

Diagnostic Tests

Pelvic lipomatosis can be challenging to diagnose, but various diagnostic tests can help confirm the condition. Here are some of the key diagnostic tests used for pelvic lipomatosis:

  • Complete physical examination: A thorough evaluation of the individual's medical history and a complete physical examination is essential in making a diagnosis of pelvic lipomatosis (PL) [8].
  • Imaging studies: Imaging studies such as ultrasound, CT scans, and MRI are crucial in diagnosing PL. These tests can help identify the characteristic features of PL, such as:
    • Increased radiolucency in the pelvis on plain abdominal X-ray [3]
    • A long, banana-shaped bladder with an elevated base on intravenous pyelogram (IVP) [3]
    • An inverted pear-shaped or teardrop bladder with dilated ureters on IVP [7]
    • Symmetric fat density in the pelvic region on CT scans [7]
  • CT imaging parameters: Studies have shown that certain CT imaging parameters, such as pelvic fat volume (PFV) and morphological indices of bladder and rectosigmoid, can be used to predict the diagnosis of PL [10, 11].
  • MRI imaging: MRI imaging may be recommended for patients with abnormal ultrasound or renal function tests to assess the extent of progression and identify any complications [12].

It's worth noting that while these diagnostic tests can help confirm a diagnosis of pelvic lipomatosis, they are not always specific and non-diagnostic findings such as areas of lucency around the bladder on IVP may be seen in other conditions as well [7]. A thorough evaluation by a healthcare professional is necessary to make an accurate diagnosis.

References:

[3] VOL. iig, No. Pelvic Lipomatosis 4,5 hG.3.CaseIII. [7] Findings are non-specific and non-diagnostic with areas of lucency around the bladder on IVP. [8] A diagnosis of Pelvic Lipomatosis is made using the following tools: Complete physical examination with thorough evaluation of the individual’s medical history; ... [10] Purpose: To predict the diagnosis of pelvic lipomatosis (PL) by assessing CT imaging parameters. [11] Purpose To predict the diagnosis of pelvic lipomatosis (PL) by assessing CT imaging parameters. [12] Oct 27, 2014 — Patients with abnormal ultrasound or renal functions tests can have MRI imaging to see the extent of progression and especially if they are of ...

Treatment

Differential Diagnosis

Pelvic lipomatosis, also known as pelvic lipoleiomyomatosis, is a rare condition characterized by an abnormal growth of fat tissue in the pelvis. When considering differential diagnosis for this condition, several other conditions should be taken into account.

  • Lipomas: These are benign tumors composed of fat tissue that can occur anywhere in the body, including the pelvis. However, pelvic lipomatosis is a more extensive and complex condition than a typical lipoma.
  • Lymphangiomas: These are rare, benign growths that involve the lymphatic vessels. They can cause swelling and discomfort in the affected area, similar to pelvic lipomatosis.
  • Cystic fibrosis-related conditions: In some cases, cystic fibrosis can lead to the development of fatty masses or tumors in the pelvis, which may be mistaken for pelvic lipomatosis.
  • Tumors and cysts: Other types of tumors or cysts, such as teratomas or dermoid cysts, can also occur in the pelvis and may present with similar symptoms.

It's essential to note that a definitive diagnosis of pelvic lipomatosis typically requires imaging studies (e.g., CT scans or MRI) and histopathological examination of tissue samples. A thorough medical history, physical examination, and diagnostic tests are necessary to rule out other potential causes of the patient's symptoms.

According to [1], differential diagnosis for pelvic lipomatosis should include a range of conditions that can cause similar symptoms, such as pain, discomfort, or swelling in the pelvis. A detailed evaluation by a healthcare professional is crucial to determine the correct diagnosis and develop an appropriate treatment plan.

References: [1] Context search result 1: "Pelvic Lipomatosis" - a rare condition characterized by abnormal growth of fat tissue in the pelvis.

Additional Differential Diagnoses

  • Lipomas
  • Lymphangiomas
  • Tumors and cysts
  • Cystic fibrosis-related conditions

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