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angioma serpiginosum
ICD-10 Codes
Related ICD-10:
Description
Angioma Serpiginosum: A Rare Vascular Anomaly
Angioma serpiginosum is a rare vascular anomaly characterized by the presence of small, superficial blood vessels near the skin surface. It presents as small red dots (puncta) that cluster together to form a linear or snake-like array (serpiginous pattern) or ring-shaped (gyrate) pattern [1]. This condition does not involve bleeding, inflammation, or pigmentation.
Key Features
- Small blood vessels near the skin surface
- Presents as small red dots (puncta) in clusters or linear arrays
- No bleeding, inflammation, or pigmentation involved
- Typically affects young females, with a rare occurrence in males [5][7]
Pathogenesis and Diagnosis
The pathogenesis of angioma serpiginosum is still unknown. It is characterized by the onset of vascular reddish macules and papules [9]. The condition is usually diagnosed based on clinical presentation and histopathological examination.
References
[1] Context result 1: Describes angioma serpiginosum as a skin condition with small blood vessels near the skin surface. [3] Context result 2: Mentions that angioma serpiginosum was first described by Hutchinson in 1889 and named by Crocker in 1894. [5] Context result 5: States that angioma serpiginosum is a rare vascular nevoid disorder due to ectatic dilation of capillaries in the papillary dermis, found almost exclusively in females. [7] Context result 7: Mentions that angioma serpiginosum is a benign vascular malformation that usually presents within the first two decades of life, more common in young females.
Additional Characteristics
- a rare vascular anomaly characterized by small superficial blood vessels near the skin surface
- small red dots (puncta) that cluster together to form a linear or snake-like array (serpiginous pattern)
- typically affects young females, with a rare occurrence in males
- is a benign vascular malformation that usually presents within the first two decades of life
Signs and Symptoms
Angioma Serpiginosum Signs and Symptoms
Angioma serpiginosum, a rare cutaneous vascular nevus, presents with distinct signs and symptoms. The condition typically affects the lower limbs, but can occur anywhere on the body.
- Early Childhood Onset: Angioma serpiginosum usually begins in early childhood as one or more small lesions that grow over a period of months or years [1].
- Lesion Characteristics: The lesions are often asymptomatic and may appear as small areas of red or violet-colored macules and papules that start to coalesce over time [7]. They can be variably compressible, with no signs of inflammation, hemorrhage, or hemosiderin pigmentation [4].
- Typical Locations: Angioma serpiginosum most often affects the buttocks and legs, but can also occur on other areas such as the face, hands, feet, and mucous membranes [3][5].
- Progression: As a child reaches puberty, the patches typically stop growing and remain unchanged [1].
It's essential to note that angioma serpiginosum is usually asymptomatic, with no bleeding, discomfort, or inflammation related to the lesions. However, in some cases, the condition may present with sporadic symptoms.
References:
[1] Context 1 [3] Context 3 [4] Context 4 [5] Context 5 [7] Context 7
Diagnostic Tests
Diagnostic Tests for Angioma Serpiginosum
Angioma serpiginosum, a rare benign vascular disorder, can be diagnosed through various tests and evaluations. Here are some of the diagnostic tests used to confirm the condition:
- Clinical Examination: A dermatologist typically identifies angioma serpiginosum based on its distinct clinical presentation, which includes multiple minute, red to purple, grouped macules in serpiginous and gyrate patterns [1].
- Dermoscopy: Dermoscopy is a non-invasive diagnostic tool that uses magnification to examine the skin. It can help confirm the diagnosis by revealing the typical clusters of dilated, thickened, and PAS+ capillaries in angioma serpiginosum [7].
- Light Microscopy: Light microscopy can also be used to confirm the diagnosis by examining the histopathological features of the condition, such as ectatic dilatation of capillaries [1].
- Imaging Studies: Imaging studies are not usually necessary to evaluate this skin lesion and are indicated only if atypical findings are present and the diagnosis is uncertain [5].
Diagnostic Teams
A diagnostic team for angioma serpiginosum may include:
- Dermatology: Dermatologists play a crucial role in diagnosing and managing angioma serpiginosum.
- Genetics: Genetic testing may be recommended to identify any underlying genetic mutations that could be contributing to the condition [12].
References
[1] Context 1: Angioma serpiginosum is a rare benign vascular disorder, characterized clinically by multiple minute, red to purple, grouped macules in serpiginous and gyrate patterns and histopathologically by ectatic dilatation of capillaries.
[5] Context 5: Apr 16, 2021 — Imaging studies are not usually necessary to evaluate this skin lesion and are indicated only if atypical findings are present and the diagnosis is uncertain.
[7] Context 7: by L Tognetti · 2024 — The clinical examination of CPH usually reveals typical clusters of dilated, thickened, and PAS+ capillaries in angioma serpiginosum.
Note: The references provided are based on the context information retrieved from a search engine.
Additional Diagnostic Tests
- Imaging Studies
- Dermoscopy
- Clinical Examination
- Light Microscopy
Treatment
Angioma serpiginosum (AS) is a rare vascular anomaly that typically affects children and young adults. While it is usually asymptomatic, some individuals may seek treatment for cosmetic reasons or to alleviate symptoms.
Treatment Options:
- Pulsed Dye Laser (PDL) Therapy: Studies have shown that PDL therapy can be effective in treating AS, with significant improvement in appearance after multiple sessions [1][2]. The pulsed dye laser works by targeting the abnormal blood vessels and reducing their size.
- KTP Laser Therapy: A novel 532 nm potassium-titanyl phosphate (KTP) laser has been used to treat AS, resulting in near complete resolution after several sessions [3].
- Intense Pulsed Light (IPL) Therapy: IPL has also been used to treat venous malformations, infantile hemangioma, and other vascular anomalies, including AS [4].
Optimal Therapeutic Approach:
While treatment is usually unnecessary for AS, reassurance is key. If treatment is desired, improvement can be achieved with PDL or KTP laser therapy after multiple sessions.
- Reassurance: In most cases, AS does not require treatment and can be managed with reassurance.
- Treatment: If treatment is desired, PDL or KTP laser therapy may be considered to improve appearance.
References:
[1] Madan V, August PJ, Ferguson JE. Pulsed-dye laser treatment of angioma serpiginosum. Clin Exp Dermatol. 2009 Jul;34(5):e186-8.
[2] CC LONG · 1997 · Cited by 51 — The results suggest that treatment using the pulsed dye laser is very effective for AS and, in most patients, produces an excellent cosmetic result.
[3] A Diociaiuti · 2019 — A novel 532 nm potassium-titanyl phosphate (KTP) laser has been used to treat AS, resulting in near complete resolution after several sessions.
[4] by A Diociaiuti · 2019 — IPL has also been used to treat venous malformations, infantile hemangioma, and other vascular anomalies, including AS.
Recommended Medications
- Pulsed Dye Laser (PDL) Therapy
- KTP Laser Therapy
- Intense Pulsed Light (IPL) Therapy
💊 Drug information is sourced from ChEBI (Chemical Entities of Biological Interest) database. Always consult with a healthcare professional before starting any medication. Click on any medication name for detailed information.
Differential Diagnosis
Differential Diagnoses for Angioma Serpiginosum
Angioma serpiginosum, a rare vascular nevoid disorder, can sometimes be mistaken for other conditions. Differentiating it from these differential diagnoses is crucial to ensure appropriate management and treatment.
- Pigmented Purpuric Dermatoses: These are usually symptomatic, bilateral, and have evidence of inflammation on skin biopsy [1]. They can present with similar clinical features as angioma serpiginosum.
- Unilateral Nevoid Telangiectasia (UNT): This condition is characterized by telangiectatic lesions that typically affect one side of the body. While it shares some similarities with angioma serpiginosum, UNT does not blanch with diascopy and has distinct dermoscopic features [12].
- Angiokeratomas: These are benign vascular lesions that can present as small, red or purple spots on the skin. They may be confused with angioma serpiginosum due to their similar appearance.
- Cutaneous Metastases: In rare cases, angioma serpiginosum can be mistaken for cutaneous metastases, particularly if the lesions are large and have a characteristic "snake-like" or "gyrate" pattern [13].
- Port-Wine Stain: This is a congenital vascular malformation that can present with similar clinical features as angioma serpiginosum. However, port-wine stain typically affects one side of the body and has distinct histological features.
It's essential to note that accurate diagnosis of angioma serpiginosum requires careful clinical evaluation, dermoscopic examination, and histopathological analysis to rule out these differential diagnoses.
References: [1] Context reference 9 [12] Context reference 12 [13] Context reference 13
Additional Differential Diagnoses
Additional Information
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