intrahepatic bile duct cystadenoma

Intrahepatic Bile Duct Cystadenoma: A Rare Benign Tumor

Intrahepatic bile duct cystadenoma (IBC) is a rare benign tumor that originates from the bile duct epithelium. It is characterized by a cystic mass within the liver, which can be unilocular or multilocular in appearance.

Key Features:

• Rare occurrence: IBC accounts for only 5% of reported cystic lesions of the liver [1].
• Benign but potentially malignant: While most IBCs are benign, they have the potential to become malignant (biliary cystadenocarcinoma) [7].
• Cystic mass: IBC presents as a cystic mass within the liver, which can be unilocular or multilocular in appearance [3][4].
• Mucus-secreting epithelium: The tumor is lined by mucus-secreting epithelium, which is a distinct histological feature of IBC-MS [9].

Diagnosis and Imaging:

• Imaging studies: Hepatic MRI can help guide the diagnosis of IBC by providing detailed images of the cystic mass within the liver [6].
• Misdiagnosis: IBCs are often misdiagnosed as simple liver cysts or hydatid disease due to their similar appearance on imaging studies [8].

References:

[1] RM Xu (2020) - Biliary cystadenoma is a rare benign tumor, accounting for only 5% of reported cystic lesions of the liver. [2] Y Yang (2022) - IBC has carcinogenic potential and originates from the bile duct epithelium. [3] Sep 22, 2020 - Biliary cystadenoma can appear as a unilocular or multilocular cystic intrahepatic mass. [4] Aug 16, 2024 - Biliary cystadenomas are cystic neoplasms that may be either unilocular or multilocular. [5] RM Xu (2020) - Biliary cystadenoma is a rare benign tumor, accounting for only 5% of reported cystic lesions of the liver. [6] Y Tlili (2024) - Hepatic MRI can help guide the diagnosis of biliary cystadenoma. [7] Y Tang (2021) - Biliary cystadenomas are rare cystic tumors of the biliary system, most of which are benign but may also be malignant. [8] Z Ahmad (2017) - Intrahepatic biliary cystadenomas are rare hepatic neoplasms, which are usually cystic and often misdiagnosed as simple liver cysts or hydatid disease. [9] W Davies (1999) - The distinct histological features of IBC-MS include a cyst lining of columnar-to-cuboidal, non-ciliated, mucin-secreting epithelium.