ICD-10: N07

Hereditary nephropathy, not elsewhere classified

Additional Information

Approximate Synonyms

ICD-10 code N07 refers to "Hereditary nephropathy, not elsewhere classified." This classification encompasses various hereditary kidney diseases that do not fall under more specific categories. Below are alternative names and related terms associated with this code:

Alternative Names

  1. Hereditary Kidney Disease: A broad term that includes any kidney disorder passed down through families.
  2. Genetic Nephropathy: Refers to kidney diseases caused by genetic mutations.
  3. Familial Nephropathy: Indicates kidney diseases that occur in families, suggesting a hereditary component.
  4. Inherited Nephropathy: A term emphasizing the genetic inheritance of kidney diseases.
  1. Nephronophthisis: A genetic disorder characterized by kidney cysts and progressive kidney failure.
  2. Alport Syndrome: A hereditary condition that affects the kidneys, ears, and eyes, often leading to kidney failure.
  3. Fabry Disease: A genetic disorder that can lead to kidney damage among other systemic issues.
  4. Cystinosis: A rare genetic disorder that leads to the accumulation of cystine within lysosomes, affecting kidney function.
  5. Congenital Nephrotic Syndrome: A group of inherited disorders that cause nephrotic syndrome in infants and young children.

Clinical Context

Hereditary nephropathies can manifest in various ways, often leading to chronic kidney disease or end-stage renal failure. The classification under N07 is essential for healthcare providers to identify and manage these conditions effectively. Understanding the alternative names and related terms can aid in better communication among healthcare professionals and improve patient care.

In summary, the ICD-10 code N07 encompasses a range of hereditary kidney diseases, and recognizing the alternative names and related terms can enhance understanding and treatment approaches for these conditions.

Related Information

Approximate Synonyms

  • Hereditary Kidney Disease
  • Genetic Nephropathy
  • Familial Nephropathy
  • Inherited Nephropathy
  • Nephronophthisis
  • Alport Syndrome
  • Fabry Disease
  • Cystinosis
  • Congenital Nephrotic Syndrome

Coding Guidelines

Excludes 2

  • Alport's syndrome (Q87.81-)
  • non-neuropathic heredofamilial amyloidosis (E85.-)
  • hereditary amyloid nephropathy (E85.-)
  • nail patella syndrome (Q87.2)

Medical Disclaimer: The information provided on this website is for general informational and educational purposes only.

It is not intended to be a substitute for professional medical advice, diagnosis, or treatment. Always seek the advice of your physician or other qualified healthcare provider with questions about your medical condition.